原著論文

2022年

Hayashi T, Matsushita T, Hisahara S, Iwahara N, Kuno A, Kunimoto R, Hosoda R, Tanno M, Shimohama S, Horio Y.
Ubiquitin-dependent rapid degradation conceals a cell-protective function of cytoplasmic SIRT3 against oxidative stress. J Biochem. 2022 Feb 21;171(2):201-213.

Iwahara N, Azekami K, Hosoda R, Nojima I, Hisahara S, Kuno A.
Activation of SIRT1 promotes membrane resealing via cortactin. Sci Rep. 2022 Sep 12;12(1):15328.

Hirose B, Ikeda K, Yamamoto D, Tsuda E, Yamauchi R, Hozuki T, Masuda Y, Imai T.
Measurement of excitation-contraction coupling time in critical illness myopathy. Clin Neurophysiol. 2022;135:30-36.

Tanemoto M, Oda R, Toyama Y, Shizukawa H, Yokokawa K, Saito T, Suzuki S, Matsumura A, Hisahara S. Intern Med. 2022;61:3605-3609.
Anti-signal Recognition Particle Antibody-positive Immune-mediated Myopathy after mRNA-1273 SARS-CoV-2 Vaccination.

Ikeda K, Yamamoto D, Usui K, Takeuchi H, Oka N, Katoh N, Yazaki M, Kametani F, Nishino I, Hisahara S.
A Case of Transthyretin Variant Amyloidosis with a TTR A97D (p.A117D) Mutation Manifesting Remarkable Asymmetric Neuropathy. Intern Med. 2022; Online ahead of print.

Yamamoto M, Manabe T, Yokokawa K, Tsuzaka K, Yamada M, Miyanaga R, Saito T, Yamamoto D, Matsumura A, Suzuki S, Hisahara S.
A Case of Cerebral Tuberculoma Diagnosed by Nested Polymerase Chain Reaction of a Formalin-fixed Paraffin-embedded Brain Biopsy Sample. Intern Med. 2022; Online ahead of print.

宮永 怜, 田中 真理子, 野中 隆行, 静川 裕彦, 下濱 俊.
病初期より慢性偽性腸閉塞を合併したmitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes(MELAS)の1例. 臨床神経学 2022; 62: 464−468.

野中 隆行, 蛭子 育美, 大橋 一慶, 静川 裕彦, 下濱 俊.
切除困難な胸腺腫を伴うMorvan症候群に化学療法が寄与した1例. 臨床神経学 2022; 62: 615−620.

2021年

Hisahara S, Iwahara N, Matsushita T, Suzuki S, Matsumura A, Fujikura M, Yokokawa K, Saito T, Manabe T, Kawamata J, Horio Y, Shimohama S.
SIRT1 decelerates morphological processing of oligodendrocyte cell lines and regulates the expression of cytoskeleton-related oligodendrocyte proteins. Biochem Biophys Res Commun. 2021 Mar 26;546:7-14.

Ikeda K, Hirose B, Yamamoto D, Hisahara S, Shimohama S, Shiraishi H, Imai T.
A case presenting electrophysiological and immunological characteristics of Fisher syndrome and Lambert-Eaton myasthenic syndrome. Muscle Nerve. 2021;63:E16-E18.

Nakamura Y, Uemura T, Kawata Y, Hirose B, Yamauchi R, Shimohama S.
Streptococcus oralis Meningitis with Gingival Bleeding in a Patient: A Case Report and Review of the Literature. Intern Med. 2021;60:789-793.

Tanemoto M, Hisahara S, Ikeda K, Yokokawa K, Manabe T, Tsuda R, Yamamoto D, Matsushita T, Matsumura A, Suzuki S, Shimohama S.
Sporadic Amyotrophic Lateral Sclerosis Due to a FUS P525L Mutation with Asymmetric Muscle Weakness and Anti-ganglioside Antibodies. Intern Med. 2021;60:1949-1953.

Hisahara S, Nishiyama A, Tsuda E, Suzuki S, Matsumura A, Ishikawa A, Sakurai A, Motoike IN, Aoki M, Aoki Y, Shimohama S.
Possible Somatic Mosaicism of Novel FUS Variant in Familial Amyotrophic Lateral Sclerosis. Neurol Genet. 2021 Jan 12;7(1):e552.

山本 大輔, 山田 稔, 曹 博, 鈴木 秀一郎, 久原 真, 下濱 俊.
神経反復刺激試験で異常減衰を認め, 小脳失調を合併したfacial-onset sensory and motor neuronopathy (FOSMN)の1例. 臨床神経学 2021; 61: 115−119.

山本 大輔, 小田 亮介, 久原 真, 石川 亜貴, 荻 朋男, 下濱 俊.
脊髄性筋萎縮症様の臨床症状を呈した MORC2 S87L 変異による Charcot-Marie-Tooth 病 2Z 型の 1 例. 臨床神経学 2021; 61: 262-264. 

小田 亮介, 藤倉 舞, 林 貴士, 松谷 学, 曽根 淳, 下濱 俊.
物忘れ発症前から MRI の経時的変化が観察された神経核内封入体病の 1 例. 臨床神経学 2021; 61:727-732. 

2020年

 Tanemoto M, Hisahara S, Hirose B, Ikeda K, Matsushita T, Suzuki S, Manabe T, Imai T, Shimohama S.
Severe Mononeuritis Multiplex Due to Rheumatoid Vasculitis in Rheumatoid Arthritis in Sustained Clinical Remission for Decades. Intern Med 2020: 59; 705-710.

Miyanaga R, Hisahara S, Ohhashi I, Yamamoto D, Matsumura A, Suzuki S, Tanimoto K, Hirakawa M, Kawamata J, Kato J, Shimohama S.
Hyperemesis-induced Wernicke-Korsakoff Syndrome due to Hypergastrinemia during Long-term Treatment with Proton Pump Inhibitors. Intern Med. 2020 Nov 1;59(21):2783-2787.

中村 祐貴, 倉内 麗徳, 高橋 明央, 山内 理香, 下濱 俊.
一側の眼瞼下垂で発症した中脳梗塞の 1 例. 臨床神経学 2020; 60: 527-532.